Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge
Vol 4 | Issue 2 | July-Dec 2018 | Page 30-32 | Yash B Rabari, Nikhil Suri, D.V. Prasad, Siddharth Shah.
Authors: Yash B Rabari [1], Nikhil Suri [1], D.V. Prasad [1], Siddharth Shah [1].
[1] Department of Orthopaedics, Rural Medical Collage, LoniBk, Maharashtra, India.
Address of Correspondence
Dr. Yash B. Rabari.
107, NRI Hostel, PMT Campus, LoniBk, Tal.-Rahta, Dist.- Ahmadnagar Maharastra 413736
Email: dryash.rabari@gmail.com
Abstract
Clear cell sarcoma (CCS) is an exceedingly rare tumor of young adults with melanocytic differentiation. The exact incidence is largely unknown, although occasional case series mention CCS comprising less than 1% of all soft tissue sarcoma. CCS is a deep-seated tumor, typically involving tendons and aponeuroses. It has a predilection for lower extremities, particularly around the foot and ankle region, accounting for nearly 40% of cases. A primary dermal origin is rarer. We report a case of primary cutaneous CCS of 42 year old female located on the left popliteal fossa. Complete excision led to relief of symptoms
Keywords: Clear cell Sarcoma, Tumor, CCS
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| How to Cite this article: Rabari YB, Suri N, Prasad D.V, Shah S. Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge . Journal of Bone and Soft Tissue Tumors July-Dec 2018;4(2): 30-32. |
