Giant Ancient Solitary Schwannoma Masquerading as Juxtacortical Osteosarcoma of Femur – A Rare Case Report and Literature Review
Vol 5 | Issue 1 | Jan-April 2019 | page: 28-30 | Julfiqar, Mohd. Aslam, Najmul Huda, Ajay Pant.
Authors: Julfiqar , Mohd. Aslam , Najmul Huda , Ajay Pant .
 Dept of Orthopaedic Surgery, Faculty of Medicine, J.N.Medical College, Aligarh Muslim University, Aligarh, India
 Department of Orthopaedics, Teerthanker Mahaveer Medical College and Research Centre, TMU, Moradabad, India
Address of Correspondence
Assistant professor, Department of Orthopaedic Surgery, Faculty of Medicine, J.N.Medical College, Aligarh Muslim University, Aligarh, India.
Introduction: Ancient schwannomas are rare variant of peripheral nerve sheath tumors characterized by the degeneration and hypocellular areas due to long-standing growth. Clinicoradiologically, these tumors can masquerade other tumors arising from the adjacent tissues. Their resemblance to malignant bone tumor has been reported very rarely in the literature. We tend to report a case of benign peripheral nerve schwannoma that greatly mimicked a juxtacortical osteosarcoma of femur.
Case Report: A 23-year-old male presented with a slow-growing painless mass with paresthesias in his right thigh for the last 2½ years. Clinically, it was suspected to be soft tissue tumor with secondary involvement of adjacent neurovascular bundle; however, plain radiograph and magnetic resonance imaging of his right thigh were suggestive of juxtacortical osteosarcoma of the right femur. Surgical exploration of the mass revealed a well-defined encapsulated mass over the anterior aspect of the right thigh, under the quadriceps muscle without infiltration into the surrounding tissue. Histopathological examination confirmed it to be an ancient schwannoma.
Results: The patient was extremely satisfied with outcomes of surgery, and he was symptom-free and there was no clinical evidence of the recurrence on subsequent follow-up.
Conclusion: A correct pre-operative diagnosis of benign peripheral nerve sheath tumors can be difficult at times. However, a slow-growing mass with the absence of other features of a malignant growth and subsequent histopathological examination including immunostaining can settle the diagnosis in almost all the cases.
Keywords: Benign, Peripheral nerve, Ancient schwannoma, Juxtacortical osteosarcoma.
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|How to Cite this article: Julfiqar, Aslam M, Huda N, Pant A. Giant Ancient Solitary Schwannoma Masquerading as Juxtacortical Osteosarcoma of Femur-A Rare Case Report and Literature Review. Journal of Bone and Soft Tissue Tumors Jan-April 2019;5(1): 28-30.|
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