Blog Elements

Half Sized Blog Element (Single Author Style)

Half Sized Blog Element (Multi Author Style)

Unusual presentation of Chordoma in distal radius

July 10, 2018

Vol 4 | Issue 2 | July-Dec 2018 | Page 33-35 | Subin Sugath, Jayashree, Shrijith MB. Authors: Subin Sugath [1], Jayashree [1], Shrijith MB [1]. [1] Dept of Regional Cancer Centre , Trivandrum. Address of Correspondence Dr. Subin Sugath Dept of Regional Cancer Centre , Trivandrum, Email:bhaskarsubin@gmail.com Abstract Chordoma is rarely seen in appendicular […]

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

July 10, 2018

Vol 4 | Issue 2 | July-Dec 2018 | Page 30-32 | Yash B Rabari, Nikhil Suri, D.V. Prasad, Siddharth Shah. Authors: Yash B Rabari [1], Nikhil Suri [1], D.V. Prasad [1], Siddharth Shah [1]. [1] Department of Orthopaedics, Rural Medical Collage, LoniBk, Maharashtra, India. Address of Correspondence Dr. Yash B. Rabari. 107, NRI Hostel, […]

Unusual presentation of Chordoma in distal radius

July 10, 2018

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

July 10, 2018

Full Sized Blog Element (Big Preview Pic)

Unusual presentation of Chordoma in distal radius

July 10, 2018

Vol 4 | Issue 2 | July-Dec 2018 | Page 33-35 | Subin Sugath, Jayashree, Shrijith MB.

Authors: Subin Sugath [1], Jayashree [1], Shrijith MB [1].

[1] Dept of Regional Cancer Centre , Trivandrum.

Address of Correspondence
Dr. Subin Sugath
Dept of Regional Cancer Centre , Trivandrum,
Email:bhaskarsubin@gmail.com

Abstract

Chordoma is rarely seen in appendicular skeleton. Here we describe a rare case of chordoma occuring in distal radius. Radiograph showed ill defined lytic distal radius, meta diaphyseal lesion. IHC marker for Chordoma Brachyury was done (TMH , Mumbai), which came diffuse strongly positive- confirming the pre op diagnosis of Extra Axial Chordoma. He was treated with Wide resection of the distal radius and one bone forearm wrist arthrodesis
Keywords: Chordoma, extraxial, radius

References

1. Walcott BP, Nahed BV, Mohyeldin A, Coumans JV, Kahle KT, Ferreira MJ. Chordoma: current concepts, management, and future directions. Lancet Oncol. 2012 Feb;13(2):e69-76.

2. Nielsen GP, Mangham DC, Grimer RJ, Rosenberg AE. Chordoma periphericum: a case report. Am J Surg Pathol 2001;25:263–7.
3. O’donnell P, Tirabosco R, Vujovic S, Bartlett W, Briggs TW, Henderson S, et al. Diagnosing an extraaxial chordoma of the proximal tibia with the help of brachyury, a molecule required for notochordal differentiation. Skeletal Radiol 2007;36:59–65.
4. Tirabosco R, Mangham DC, Rosenberg AE, Vujovic S, Bousdras K, Pizzolitto S, et al. Brachyury expression in extra-axial skeletal and soft tissue chordomas: a marker that distinguishes chordoma from mixed tumour/myoepithelioma/parachordoma in soft tissue. Am J Surg Pathol 2008;32:572–80.
5. van Akkooi AC, van Geel AN, Bessems JH, den Bakker MA. Extra-axial chordoma. J Bone Joint Surg Br 2006;88:1232–4.
6. DiFrancesco LM, Davanzo Castillo CA, Temple WJ. Extra-axial chordoma. Arch Pathol Lab Med 2006; 130:1871–4.
7. Lantos JE, Agaram NP, Healey JH, Hwang S. Recurrent skeletal extra-axial chordoma confirmed with brachyury: imaging features and review of the literature. Skeletal Radiol 2013;42:1451–9
8. Rekhi B. Primary, large extra-axial chordoma in proximal tibia: a rare case report with literature review and diagnostic implications. APMIS. 2016
Mar;124(3):238-42

How to Cite this article: Sugath S, Jayashree, Shrijith MB. Unusual presentation of Chordoma in distal radius. Journal of Bone and Soft Tissue Tumors July-Dec 2018;4(2): 33-35.

(Abstract Full Text HTML) (Download PDF)

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

July 10, 2018

Vol 4 | Issue 2 | July-Dec 2018 | Page 30-32 | Yash B Rabari, Nikhil Suri, D.V. Prasad, Siddharth Shah.

Authors: Yash B Rabari [1], Nikhil Suri [1], D.V. Prasad [1], Siddharth Shah [1].

[1] Department of Orthopaedics, Rural Medical Collage, LoniBk, Maharashtra, India.

Address of Correspondence
Dr. Yash B. Rabari.
107, NRI Hostel, PMT Campus, LoniBk, Tal.-Rahta, Dist.- Ahmadnagar Maharastra 413736
Email: dryash.rabari@gmail.com

Abstract

Clear cell sarcoma (CCS) is an exceedingly rare tumor of young adults with melanocytic differentiation. The exact incidence is largely unknown, although occasional case series mention CCS comprising less than 1% of all soft tissue sarcoma. CCS is a deep-seated tumor, typically involving tendons and aponeuroses. It has a predilection for lower extremities, particularly around the foot and ankle region, accounting for nearly 40% of cases. A primary dermal origin is rarer. We report a case of primary cutaneous CCS of 42 year old female located on the left popliteal fossa. Complete excision led to relief of symptoms
Keywords: Clear cell Sarcoma, Tumor, CCS

References

1. Dim DC, Cooley LD, Miranda RN. Clear cell sarcoma of tendons and aponeuroses: A review. Arch Pathol Lab Med. 2007;131:152–6.
2. Deenik W, Mooi WJ, Rutgers EJ, Peterse JL, Hart AA, Kroon BB. Clear cell sarcoma (malignant melanoma) of soft parts: A clinicopathological study of 30 cases. Cancer. 1999;86:969–75.
3. Kazakos CJ, Galanis VG, Giatromanolaki A, Verettas DA, Sivridis E. Clear cell sarcoma of the scapula. A case report and review of literature. World J SurgOncol. 2006;4:48–53. [PMC free article]
4. Hantschke M, Mentzel T, Rutten A, Palmedo G, Calonje E, Lazar AJ, et al. Cutaneous clear cell sarcoma: A clinicopathological, immunohistochemical, and molecular analysis of 12 cases emphasizing its distinction form dermal melanoma. Am J SurgPathol. 2010;34:216–22.
5. Hisaoka M, Ishida T, Kuo TT, Matsuyama A, Imamura T, Nishida K, et al. Clear cell sarcoma of soft tissue: A clinicopathological, immunohistochemical, and molecular analysis of 33 cases. Am J SurgPathol. 2008;32:452–60.
6. Patel RM, Downs-Kelly E, Weiss SW, Folpe AL, Tubbs RR, Tuthill RJ, et al. Dual-color, break-apart fluorescence in situ hybridization for EWS gene rearrangement distinguishes clear cell sarcoma of soft tissue from malignant melanoma. Mod Pathol. 2005;18:1585–90.
7. Rodriguez-Martin M, Saez- Rodriguez M, Esquivel B, Gonzalez RS, Cabrera AN, Herrera AM. Clear cell sarcoma: A case mimicking primary cutaneous malignant melanoma. Indian J Dermatol. 2009;54:168–72.
8. Enzinger FM. Clear cell sarcoma of tendons and aponeuroses: An analysis of 21 cases. Cancer. 1965;18:1163–74.
9. Chung EB, Enzinger FM. Malignant melanoma of soft parts.A reassessment of clear cell sarcoma. Am J SurgPathol. 1983;7:405–13.

How to Cite this article: Rabari YB, Suri N, Prasad D.V, Shah S. Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge . Journal of Bone and Soft Tissue Tumors July-Dec 2018;4(2): 30-32.

Half Sized Blog Element (Single Author Style)

Half Sized Blog Element (Multi Author Style)

Unusual presentation of Chordoma in distal radius

Like this:

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

Like this:

Unusual presentation of Chordoma in distal radius

Like this:

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

Like this:

Full Sized Blog Element (Big Preview Pic)

Unusual presentation of Chordoma in distal radius

Authors: Subin Sugath [1], Jayashree [1], Shrijith MB [1].

Abstract

References

(Abstract Full Text HTML) (Download PDF)

Like this:

Clear Cell Sarcoma: A Rare Aggressive Tumor with Potential Diagnostic Challenge

Authors: Yash B Rabari [1], Nikhil Suri [1], D.V. Prasad [1], Siddharth Shah [1].

Abstract

References

(Abstract Full Text HTML) (Download PDF)

Like this:

Like this:

Journal of Bone and Soft Tissue Tumors (JBST) Editorial Office

Important Information

Journal of Bone and Soft Tissue Tumors (JBST) License

Half Sized Blog Element (Single Author Style)

Half Sized Blog Element (Multi Author Style)

Like this:

Like this:

Like this:

Like this:

Full Sized Blog Element (Big Preview Pic)

Authors: Subin Sugath [1], Jayashree [1], Shrijith MB [1].

Abstract

References

(Abstract Full Text HTML) (Download PDF)

Like this:

Authors: Yash B Rabari [1], Nikhil Suri [1], D.V. Prasad [1], Siddharth Shah [1].

Abstract

References

(Abstract Full Text HTML) (Download PDF)

Like this:

Share this:

Like this:

Journal of Bone and Soft Tissue Tumors (JBST) Editorial Office

Important Information

Journal of Bone and Soft Tissue Tumors (JBST) License