Vol 4 | Issue 2 | July-Dec 2018 | Page 33-35 | Subin Sugath, Jayashree, Shrijith MB.<\/p>\n
[1] Dept of Regional Cancer Centre , Trivandrum.<\/p>\n
Address of Correspondence<\/span><\/strong> Chordoma is rarely seen in appendicular skeleton. Here we describe a rare case of chordoma occuring in distal radius. Radiograph showed ill defined lytic distal radius, meta diaphyseal lesion. IHC marker for Chordoma Brachyury was done (TMH , Mumbai), which came diffuse strongly positive- confirming the pre op diagnosis of Extra Axial Chordoma. He was treated with Wide resection of the distal radius and one bone forearm wrist arthrodesis 1. Walcott BP, Nahed BV, Mohyeldin A, Coumans JV, Kahle KT, Ferreira MJ. Chordoma: current concepts, management, and future directions. Lancet Oncol. 2012 Feb;13(2):e69-76.<\/p>\n 2. Nielsen GP, Mangham DC, Grimer RJ, Rosenberg AE. Chordoma periphericum: a case report. Am J Surg Pathol 2001;25:263\u20137.
\nDr. Subin Sugath
\nDept of Regional Cancer Centre , Trivandrum,
\nEmail:bhaskarsubin@gmail.com<\/p>\n
\nAbstract<\/strong><\/span><\/h3>\n
\nKeywords:<\/span><\/strong> Chordoma, extraxial, radius<\/p>\n
\nReferences<\/span><\/h3>\n
\n3. O’donnell P, Tirabosco R, Vujovic S, Bartlett W, Briggs TW, Henderson S, et al. Diagnosing an extraaxial chordoma of the proximal tibia with the help of brachyury, a molecule required for notochordal differentiation. Skeletal Radiol 2007;36:59\u201365.
\n4. Tirabosco R, Mangham DC, Rosenberg AE, Vujovic S, Bousdras K, Pizzolitto S, et al. Brachyury expression in extra-axial skeletal and soft tissue chordomas: a marker that distinguishes chordoma from mixed tumour\/myoepithelioma\/parachordoma in soft tissue. Am J Surg Pathol 2008;32:572\u201380.
\n5. van Akkooi AC, van Geel AN, Bessems JH, den Bakker MA. Extra-axial chordoma. J Bone Joint Surg Br 2006;88:1232\u20134.
\n6. DiFrancesco LM, Davanzo Castillo CA, Temple WJ. Extra-axial chordoma. Arch Pathol Lab Med 2006; 130:1871\u20134.
\n7. Lantos JE, Agaram NP, Healey JH, Hwang S. Recurrent skeletal extra-axial chordoma confirmed with brachyury: imaging features and review of the literature. Skeletal Radiol 2013;42:1451\u20139
\n8. Rekhi B. Primary, large extra-axial chordoma in proximal tibia: a rare case report with literature review and diagnostic implications. APMIS. 2016
\nMar;124(3):238-42<\/p>\n
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